翻訳と辞書 Words near each other ・ Glodeni District ・ Glodeni River ・ Glodeni, Dâmbovița ・ Glodeni, Mureș ・ Glodesind ・ Glodișor River ・ Glodoasa River ・ Glodok ・ Glodu ・ Glodu River ・ Glodu River (Almaș) ・ Glodu River (Azuga) ・ Globostomia pervicax ・ Globosusa ・ Globothalamea ・ Globotriaosylceramide ・ Globotriaosylceramide 3-beta-N-acetylgalactosaminyltransferase ・ Globotriosylceramide b-1,6-N-acetylgalactosaminyl-transferase ・ Globotype ・ Globovisión ・ Globovula ・ Globovula cavanaghi ・ Globovula sphaera ・ Globočdol ・ Globoče ・ Globočec Ludbreški ・ Globočica ・ Globočice pri Kostanjevici ・ Globočice, Brežice ・ Globrix Dictionary Lists mini英和辞書 mini和英辞書 Webster 1913 Latin-English FOLDOC Wikipedia English ウィキペディア

翻訳と辞書　辞書検索 [ 開発暫定版 ] スポンサード リンク Globotriaosylceramide ： ウィキペディア英語版 Globotriaosylceramide Globotriaosylceramide is a ganglioside. It is also known as CD77, Gb3, and ceramide trihexoside. It is one of the few clusters of differentiation that is not a protein. It is formed by the alpha linkage of galactose to lactosylceramide catalyzed by A4GALT. It is metabolized by alpha-galactosidase, which hydrolyzes the terminal alpha linkage. ==Clinical significance== Defects in the enzyme alpha-galactosidase lead to the build up of globotriaosylceramide, causing Fabry's disease.〔Desnick RJ, Ioannou YA, Eng CM. a-Galactosidase A deficiency: Fabry disease. In: Scriver CR, Beaudet AL, Sly WS, Valle D, eds. The metabolic & molecular bases of inherited disease. 8th ed. Vol. 3. New York: McGraw-Hill, 2001:3733-74.〕 Globotriaosylceramide is also one of the targets of Shiga toxin, which is responsible for pathogenicity of enterohemorrhagic Escherichia coli (EHEC). 抄文引用元・出典: フリー百科事典『 ウィキペディア（Wikipedia）』 ■ウィキペディアで「Globotriaosylceramide」の詳細全文を読む スポンサード リンク 翻訳と辞書 : 翻訳のためのインターネットリソース Copyright(C) kotoba.ne.jp 1997-2016. All Rights Reserved.