翻訳と辞書
Words near each other
・ N-Acetylgalactosamine
・ N-acetylgalactosamine 4-sulfate 6-O-sulfotransferase
・ N-acetylgalactosamine kinase
・ N-acetylgalactosamine-4-sulfatase
・ N-acetylgalactosamine-6-sulfatase
・ N-acetylgalactosamine-N,N'-diacetylbacillosaminyl-diphospho-undecaprenol 4-alpha-N-acetylgalactosaminyltransferase
・ N-acetylgalactosaminoglycan deacetylase
・ N-acetylgalactosaminyl-proteoglycan 3-beta-glucuronosyltransferase
・ N-Acetylglucosamine
・ N-acetylglucosamine deacetylase
・ N-acetylglucosamine kinase
・ N-Acetylglucosamine receptor
・ N-acetylglucosamine-1-phosphate transferase
・ N-acetylglucosamine-1-phosphodiester alpha-N-acetylglucosaminidase
・ N-acetylglucosamine-6-phosphate deacetylase
N-acetylglucosamine-6-sulfatase
・ N-acetylglucosaminyl-diphospho-decaprenol L-rhamnosyltransferase
・ N-acetylglucosaminyl-proteoglycan 4-beta-glucuronosyltransferase
・ N-acetylglucosaminyldiphosphodolichol N-acetylglucosaminyltransferase
・ N-acetylglucosaminyldiphosphoundecaprenol glucosyltransferase
・ N-acetylglucosaminyldiphosphoundecaprenol N-acetyl-beta-D-mannosaminyltransferase
・ N-acetylglucosaminylphosphatidylinositol deacetylase
・ N-acetylglucosaminyltransferase I
・ N-Acetylglutamate synthase
・ N-Acetylglutamate synthase deficiency
・ N-acetylglutamate synthetase
・ N-Acetylglutamic acid
・ N-Acetylglycinamide
・ N-acetylhexosamine 1-dehydrogenase
・ N-acetylhexosamine 1-kinase


Dictionary Lists
翻訳と辞書 辞書検索 [ 開発暫定版 ]
スポンサード リンク

N-acetylglucosamine-6-sulfatase : ウィキペディア英語版
N-acetylglucosamine-6-sulfatase

N-acetylglucosamine-6-sulfatase also known as glucosamine (N-acetyl)-6-sulfatase is an enzyme that in humans is encoded by the GNS gene. This enzyme is deficient in Sanfilippo Syndrome type IIId. This enzyme catalyses the following chemical reaction:
: Hydrolysis of the 6-sulfate groups of the N-acetyl-D-glucosamine 6-sulfate units of heparan sulfate and keratan sulfate
== Function ==

N-acetylglucosamine-6-sulfatase is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate.〔

抄文引用元・出典: フリー百科事典『 ウィキペディア(Wikipedia)
ウィキペディアで「N-acetylglucosamine-6-sulfatase」の詳細全文を読む



スポンサード リンク
翻訳と辞書 : 翻訳のためのインターネットリソース

Copyright(C) kotoba.ne.jp 1997-2016. All Rights Reserved.